Objective: To explore the clinical characteristics and pathogenesis of primary systemic amyloidosis. 前言:目的:探讨原发性系统性淀粉样变病的临床特点和发病机制。
Primary circumscribed amyloidosis of skin 皮肤原发性局限性淀粉样变性
The Studies of Different Kinds of Starch and Preparing Ways to the Starch-Based Wood Adhesive primary cutaneous amyloidosis 原淀粉和预处理方法对淀粉基木材胶粘剂性能的影响研究原发性皮肤淀粉样变性
Primary Hepatic Amyloidosis; A Case Report and Review Literature 原发性肝淀粉样变性1例报告并文献复习
Primary kidney amyloidosis was found in 11 cases, and secondary kidney amyloidosis in 4 cases. 原发性肾淀粉样变性11例,继发性肾淀粉样变性4例。
Objective: To investigate the role of electron microscopy ( EM) and immunoelectron microscopy ( IEM) in the diagnosis of light chain deposition diseases ( LCDD) and primary amyloidosis ( AL) of the kidney. 目的:探讨电镜及免疫电镜方法在肾轻链沉积病(lightchaindepositiondisease,LCDD)和轻链型淀粉样变(amyloid,AL)诊断中的作用。
Objective: To elevate the effect of diagnosis and treatment of this disease, the histogenesis and diagnosis and treatment of the primary amyloidosis of urinary bladder and ureters were retrospectively analysed. 目的:回顾分析原发性膀胱、输尿管淀粉样变的组织学发生、临床诊断和治疗情况,以提高对该病的诊治疗效。
Objective: To investigate the clinical feature, pathogenesis, and therapy of Primary systemic amyloidosis with acquired factor-X deficiency. 目的:探讨原发性系统性淀粉样变性并发凝血因子X缺乏的临床特征、发病机制及治疗方法。
Results 12 of the 30 cases were systemic amyloidosis. Among them 9 were primary amyloidosis, 1 secondary amyloidosis and 2 familial amyloid polyneuropathy. 结果系统性淀粉样变性12例,其中原发性9例、继发性1例、家族性2例;
Measurement of Serum IgE& IL-4 Level in Primary Amyloidosis of the Skin 原发性皮肤淀粉样变患者血清中IL-4及IgE水平测定
Objective To improve the diagnosis level of primary amyloidosis and analyze the causes of misdiagnosis. 目的总结原发性淀粉样变性病的临床资料,分析误诊情况,以期提高对此病的认识。
Four cases of typical oral and maxillofacial primary amyloidosis were reported, 3 cases had lesions on the tongue, 1 case had lesion involved in both skin and oral mucosa. It is essential to conduct general physical check-up and follow-up survey. 本组4例典型地发生于口腔颌面部的原发性淀粉样变性病例,3例病变部位为舌,1例为皮肤和口腔粘膜同时受累,临床提示有必要进行全身系统检查及追踪随访。
Conclusion: The mechanism of factor-X deficiency with primary amyloidosis was known as that the factor-X directly bind to amyloid fibrils and deposit in tissue. 结论:目前认为原发性系统性淀粉样变性并发凝血因子X缺乏的机制是淀粉样纤维与X因子特异性结合沉积在组织中形成的。
Clinical and pathological manifestations of light chain nephropathy and primary amyloidosis 轻链肾病和轻链型淀粉样变肾脏损害的临床和病理
Clinical Value of Lingual Biopsy in Diagnosis of Primary Systemic Amyloidosis 舌活检在原发性系统性淀粉样变性病诊断中的价值
Ultrastructural and immunoelectron microscopic study on light chain deposition diseases and primary amyloidosis of the kidney 肾轻链沉积病和轻链型淀粉样变的电镜及免疫电镜研究
Methods: Cardiac function of 74 patients with primary cardiac amyloidosis confirmed by biopsy were examined by echocardiography and all patients were divided into normal cardiac systolic function group and cardiac systolic function decreased group according to the examine results. 方法:对经心内膜活检证实并行超声心动图检查的74例心脏淀粉样变性患者的心脏功能变化进行分析,并根据心功能情况分收缩功能正常组和收缩功能减退组。
Objective: To study and analyse clinically 21 cases of primary systemic amyloidosis. 目的:临床研究和分析原发性系统性淀粉样变21例。
Clinical Characteristics and Diagnosis of Gastrointestinal Primary Systemic Amyloidosis 原发性系统性淀粉样变的消化系统临床表现和诊断
Radiographic findings of thorax in primary amyloidosis ( analysis of 9 cases) 原发淀粉样变病的胸部表现(附九例报告)
A case of primary systemic amyloidosis ( PSA) is reported. 报告1例原发性系统性淀粉样变病。
The Study of Histogenesis of Amyloid in Primary Cutaneous Amyloidosis 原发性皮肤淀粉样变淀粉样蛋白组织来源的研究
Objective To report a case of nodular localized primary cutaneous amyloidosis ( NLPCA). 目的报告1例结节性限局性原发性皮肤淀粉样变性。
Methods 40 cases primary amyloidosis diagnosed in our hospital from 1981 to 2001 were retrospectively analyzed. 方法回顾性对北京协和医院近20a间收治的40例原发性淀粉样变患者的临床表现、诊断及治疗情况进行分析总结。
Observation and nursing of a patient with primary systemic amyloidosis 1例原发性多系统淀粉样变性患者的观察与护理
Here we report a case of primary hepatic amyloidosis. A 63-year-old female patient with hepatosplenomegaly as the main manifestation, was confirmed the diagnosis of hepatic amyloidosis through positive liver biopsy stained with Congo red. 本文报道了一例原发性肝淀粉样变性,为63岁女性患者,以肝脾肿大为主要表现,肝脏穿刺活检病理示刚果红染色阳性,确诊为肝淀粉样变性。